Dentinogenesis Imperfecta is an autosomal dominant disease. The defect affects both deciduous and permanent teeth. There are three types of DGI. DGI type I associated with osteogenesis imperfecta (OI), DGI type II as a separate disease without OI, and DGI type III is rare and found only in Maryland (USA), otherwise known as the Brandywine type. In the clinical examination colour of the teeth varies from yellow through brown, grey to blue with an opalescent translucent shine. Radiographically, both deciduous and permanent teeth present root canals and pulp chambers with progressive obliteration short and narrow roots, and improper dentine-enamel junction. The enamel often becomes chipped away exposing poorely mineralized dentine which can lead to rapid attrition. The early detection of the disorder is essential for undertaking preventative measures and choosing appropriate treatment plan with the goal of preserving. As the condition progresses, treatment becomes more complicated and requires interdisciplinary approach.. The aim of the study is to present the methods of treatment that can be used in cases of dentinogenesis imperfecta type II, depending on the patient’s age, type of dentition and the extent of tooth destruction.